Case Reports
Vol. 43 No. 1 (2021)
Frontal bone fibrous dysplasia in a 6-months-old boy: A distinctive entity
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All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.
Received: 5 December 2019
Accepted: 2 March 2021
Accepted: 2 March 2021
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Fibrous Dysplasia (FD) is a non-malignant condition caused by post-zygotic, activating mutations of the GNAS gene that results in inhibition of the differentiation and proliferation of bone-forming stromal cells and leads to the replacement of normal bone and marrow by fibrous tissue and woven bone. The clinical behavior and progression of FD is variable. The management of this condition is difficult and in every case is strictly individualized. We report a case of frontal fibrous dysplasia in a 6month’s old boy who underwent a successfully resection of the lesion with an excellent cosmetic effect.
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Citations
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How to Cite
Frontal bone fibrous dysplasia in a 6-months-old boy: A distinctive entity. (2021). La Pediatria Medica E Chirurgica, 43(1). https://doi.org/10.4081/pmc.2021.225